No. |
薬物名(臨床試験情報から抽出) |
DrugBank |
KEGG DRUG * |
KEGG GENES * |
KEGG PATHWAY |
指定難病告示番号 * |
1 |
5,6,7,8-tetrahydrobiopterin |
Sapropterin |
D08505 |
- |
- |
1件: 240 |
2 |
6r-bh4 |
Sapropterin |
D08505 |
- |
- |
3件: 86, 124, 240 |
3 |
Amino acids |
Amino acids |
- |
- |
- |
4件: 70, 90, 240, 298 |
4 |
Bmn 165 |
- |
- |
- |
- |
1件: 240 |
5 |
Bmn 165 (ravpal-peg) |
Pegvaliase |
D11077 |
- |
- |
1件: 240 |
6 |
Bmn165 20mg/day |
- |
- |
- |
- |
1件: 240 |
7 |
Bmn165 40mg/day |
- |
- |
- |
- |
1件: 240 |
8 |
Cdx 6114 |
- |
- |
- |
- |
1件: 240 |
9 |
Cnsa-001 |
- |
- |
- |
- |
1件: 240 |
10 |
Corn |
Corn |
- |
- |
- |
2件: 46, 240 |
11 |
Corn/soy oil |
Corn |
- |
- |
- |
1件: 240 |
12 |
Diet |
- |
- |
- |
- |
2件: 240, 299 |
13 |
Dietary supplement for pku patients |
- |
- |
- |
- |
1件: 240 |
14 |
Docosahexaenoic acid |
Doconexent |
- |
- |
- |
7件: 6, 49, 90, 94, 240, 299, 301 |
15 |
Free amino acids intake |
Amino acids |
- |
- |
- |
1件: 240 |
16 |
Glycomacropeptide-based protein substitute |
- |
- |
- |
- |
1件: 240 |
17 |
High oleic sunflower oil |
Sunflower oil |
D09006 |
- |
- |
1件: 240 |
18 |
Immunosuppression |
- |
- |
- |
- |
1件: 240 |
19 |
Kuvan |
Sapropterin |
D08505 |
- |
- |
1件: 240 |
20 |
Kuvantm therapy |
- |
- |
- |
- |
1件: 240 |
21 |
Kuvan® |
- |
- |
- |
- |
1件: 240 |
22 |
Kuvan® (sapropterin dihydrochloride) |
Sapropterin |
D08505 |
- |
- |
1件: 240 |
23 |
Large neutral amino acid therapy |
- |
- |
- |
- |
1件: 240 |
24 |
Microalgal oil |
- |
- |
- |
- |
1件: 240 |
25 |
Moxifloxacin |
Moxifloxacin |
D00874, D08237 |
- |
- |
8件: 2, 6, 46, 49, 85, 86, 240, 299 |
26 |
N.a. |
- |
- |
- |
- |
8件: 3, 6, 8, 13, 46, 97, 240, 256 |
27 |
Pegvaliase |
Pegvaliase |
D11077 |
- |
- |
1件: 240 |
28 |
Phenoptin |
- |
- |
- |
- |
2件: 124, 240 |
29 |
Phenylalanine |
L-phenylalanine |
D00021 |
- |
- |
1件: 240 |
30 |
Phenylalanine-free protein substitute tablets |
L-phenylalanine |
D00021 |
- |
- |
1件: 240 |
31 |
Phenylketonuria-type diet |
- |
- |
- |
- |
1件: 240 |
32 |
Pku explore |
- |
- |
- |
- |
1件: 240 |
33 |
Pku sphere |
- |
- |
- |
- |
1件: 240 |
34 |
Pku start |
- |
- |
- |
- |
1件: 240 |
35 |
Protein intake |
- |
- |
- |
- |
1件: 240 |
36 |
Ravpal-peg |
Pegvaliase |
D11077 |
- |
- |
1件: 240 |
37 |
Rtx-134 |
- |
- |
- |
- |
1件: 240 |
38 |
Sapropterin |
Sapropterin |
D08505 |
- |
- |
3件: 86, 124, 240 |
39 |
Sapropterin (kuvan) |
Sapropterin |
D08505 |
- |
- |
1件: 240 |
40 |
Sapropterin dihydrochloride |
Sapropterin |
D08505 |
- |
- |
1件: 240 |
41 |
Sapropterin dihydrochloride, 6r-bh4, tetrahydrobiopterin |
Sapropterin |
D08505 |
- |
- |
1件: 240 |
42 |
Sapropterin dihydrocholoride |
Sapropterin |
D08505 |
- |
- |
1件: 240 |
43 |
Sapropterin hydrochloride |
Sapropterin |
D08505 |
- |
- |
1件: 240 |
44 |
Sapropterin, sapropterin dihydrochloride |
Sapropterin |
D08505 |
- |
- |
1件: 240 |
45 |
Sapropterin, sapropterin hydrochloride |
Sapropterin |
D08505 |
- |
- |
1件: 240 |
46 |
Sapropterindihydrochloride |
- |
- |
- |
- |
1件: 240 |
47 |
Saproterin dihydrochloride |
- |
- |
- |
- |
1件: 240 |
48 |
Sunflower oil |
Sunflower oil |
D09006 |
- |
- |
3件: 46, 240, 299 |
49 |
Synb1618 |
- |
- |
- |
- |
1件: 240 |
50 |
Synergy |
- |
- |
- |
- |
1件: 240 |
51 |
T1401 |
- |
- |
- |
- |
1件: 240 |
52 |
Tetrahydrobiopterin |
Sapropterin |
D08505 |
- |
- |
1件: 240 |
53 |
Tetrahydrobiopterin (bh4) |
Sapropterin |
D08505 |
- |
- |
1件: 240 |