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No.
KEGG GENES
KEGG PATHWAY
KEGG DRUG
DrugBank
指定難病告示番号
1
GUSB
6件:
Pentose and glucuronate interconversions
Pentose and glucuronate interconversions
,
Glycosaminoglycan degradation
,
Porphyrin metabolism
,
Drug metabolism - other enzymes
,
Metabolic pathways
,
Lysosome
6件:
Pentose and glucuronate interconversions
,
Glycosaminoglycan degradation
,
Porphyrin metabolism
,
D
...
D11004
D11004
Vestronidase alfa
1件:
19
19
2
HPRT1
3件:
Purine metabolism
Purine metabolism
,
Drug metabolism - other enzymes
,
Metabolic pathways
D00161
D00161
Mercaptopurine
4件:
65
65
,
96
,
97
,
164
3
HPRT1
3件:
Purine metabolism
Purine metabolism
,
Drug metabolism - other enzymes
,
Metabolic pathways
D04931
D04931
Mercaptopurine
4件:
65
65
,
96
,
97
,
164
4
HPRT1
3件:
Purine metabolism
Purine metabolism
,
Drug metabolism - other enzymes
,
Metabolic pathways
D06109
D06109
Tioguanine
2件:
13
13
,
37
5
HPRT1
3件:
Purine metabolism
Purine metabolism
,
Drug metabolism - other enzymes
,
Metabolic pathways
D08603
D08603
Tioguanine
2件:
13
13
,
37
6
IMPDH1
3件:
Purine metabolism
Purine metabolism
,
Drug metabolism - other enzymes
,
Metabolic pathways
D00752
D00752
Mycophenolate mofetil
34件:
2
2
,
11
,
13
,
19
,
20
,
28
,
35
,
36
,
42
,
43
,
44
,
45
,
49
,
51
,
53
,
60
,
61
,
62
,
65
,
66
,
85
,
93
,
95
,
96
,
162
,
164
,
222
,
224
,
226
,
234
,
283
,
284
,
285
,
300
34件:
2
,
11
,
13
,
19
,
20
,
28
,
35
,
36
,
42
,
43
,
44
,
45
,
49
,
51
,
53
,
60
,
61
,
62
,
65
,
66
,
85
,
93
,
95
,
96
, ...
7
IMPDH1
3件:
Purine metabolism
Purine metabolism
,
Drug metabolism - other enzymes
,
Metabolic pathways
D01392
D01392
Mizoribine
8件:
46
46
,
49
,
51
,
53
,
66
,
94
,
222
,
224
8
IMPDH1
3件:
Purine metabolism
Purine metabolism
,
Drug metabolism - other enzymes
,
Metabolic pathways
D05094
D05094
Mycophenolate mofetil
34件:
2
2
,
11
,
13
,
19
,
20
,
28
,
35
,
36
,
42
,
43
,
44
,
45
,
49
,
51
,
53
,
60
,
61
,
62
,
65
,
66
,
85
,
93
,
95
,
96
,
162
,
164
,
222
,
224
,
226
,
234
,
283
,
284
,
285
,
300
34件:
2
,
11
,
13
,
19
,
20
,
28
,
35
,
36
,
42
,
43
,
44
,
45
,
49
,
51
,
53
,
60
,
61
,
62
,
65
,
66
,
85
,
93
,
95
,
96
, ...
9
IMPDH1
3件:
Purine metabolism
Purine metabolism
,
Drug metabolism - other enzymes
,
Metabolic pathways
D05095
D05095
Mycophenolate mofetil
34件:
2
2
,
11
,
13
,
19
,
20
,
28
,
35
,
36
,
42
,
43
,
44
,
45
,
49
,
51
,
53
,
60
,
61
,
62
,
65
,
66
,
85
,
93
,
95
,
96
,
162
,
164
,
222
,
224
,
226
,
234
,
283
,
284
,
285
,
300
34件:
2
,
11
,
13
,
19
,
20
,
28
,
35
,
36
,
42
,
43
,
44
,
45
,
49
,
51
,
53
,
60
,
61
,
62
,
65
,
66
,
85
,
93
,
95
,
96
, ...
10
IMPDH1
3件:
Purine metabolism
Purine metabolism
,
Drug metabolism - other enzymes
,
Metabolic pathways
D05096
D05096
Mycophenolic acid
36件:
2
2
,
11
,
13
,
19
,
20
,
28
,
35
,
36
,
42
,
43
,
44
,
45
,
49
,
51
,
53
,
60
,
61
,
62
,
65
,
66
,
84
,
85
,
93
,
95
,
96
,
162
,
164
,
222
,
224
,
226
,
228
,
234
,
283
,
284
,
285
,
300
36件:
2
,
11
,
13
,
19
,
20
,
28
,
35
,
36
,
42
,
43
,
44
,
45
,
49
,
51
,
53
,
60
,
61
,
62
,
65
,
66
,
84
,
85
,
93
,
95
, ...