1 |
CTSC
| 1件: Lysosome Lysosome | D12120
D12120
|
Brensocatib
| 1件: 299 299 |
2 |
TPP1
| 1件: Lysosome Lysosome | D10813
D10813
|
Cerliponase alfa
| 1件: 19 19 |
3 |
GAA
| 3件: Starch and sucrose metabolism Starch and sucrose metabolism, Metabolic pathways, Lysosome | D00216
D00216
|
Acarbose
| 1件: 298 298 |
4 |
GAA
| 3件: Starch and sucrose metabolism Starch and sucrose metabolism, Metabolic pathways, Lysosome | D03207
D03207
|
Alglucosidase alfa
| 1件: 256 256 |
5 |
GAA
| 3件: Starch and sucrose metabolism Starch and sucrose metabolism, Metabolic pathways, Lysosome | D09605
D09605
|
Duvoglustat
| 1件: 256 256 |
6 |
GAA
| 3件: Starch and sucrose metabolism Starch and sucrose metabolism, Metabolic pathways, Lysosome | D11744
D11744
|
Avalglucosidase alfa
| 1件: 256 256 |
7 |
GAA
| 3件: Starch and sucrose metabolism Starch and sucrose metabolism, Metabolic pathways, Lysosome | D11798
D11798
|
Cipaglucosidase alfa
| 1件: 256 256 |
8 |
GALNS
| 2件: Metabolic pathways Metabolic pathways, Lysosome | D10333
D10333
|
Elosulfase alfa
| 1件: 19 19 |
9 |
GBA
| 4件: Other glycan degradation Other glycan degradation, Sphingolipid metabolism, Metabolic pathways, Lysosome | D02810
D02810
|
Alglucerase
| 1件: 19 19 |
10 |
GBA
| 4件: Other glycan degradation Other glycan degradation, Sphingolipid metabolism, Metabolic pathways, Lysosome | D03020
D03020
|
Imiglucerase
| 1件: 19 19 |
11 |
GBA
| 4件: Other glycan degradation Other glycan degradation, Sphingolipid metabolism, Metabolic pathways, Lysosome | D09029
D09029
|
Velaglucerase alfa
| 1件: 19 19 |
12 |
GBA
| 4件: Other glycan degradation Other glycan degradation, Sphingolipid metabolism, Metabolic pathways, Lysosome | D09675
D09675
|
Taliglucerase alfa
| 1件: 19 19 |
13 |
GLA
| 3件: Sphingolipid metabolism Sphingolipid metabolism, Metabolic pathways, Lysosome | D02784
D02784
|
Agalsidase alfa
| 1件: 19 19 |
14 |
GLA
| 3件: Sphingolipid metabolism Sphingolipid metabolism, Metabolic pathways, Lysosome | D03228
D03228
|
Agalsidase beta
| 1件: 19 19 |
15 |
GUSB
| 4件: Pentose and glucuronate interconversions Pentose and glucuronate interconversions, Porphyrin metabolism, Metabolic pathways, Lysosome | D11004
D11004
|
Vestronidase alfa
| 1件: 19 19 |
16 |
IDS
| 2件: Metabolic pathways Metabolic pathways, Lysosome | D04499
D04499
|
Idursulfase
| 1件: 19 19 |
17 |
IDS
| 2件: Metabolic pathways Metabolic pathways, Lysosome | D11025
D11025
|
Idursulfase beta
| 1件: 19 19 |
18 |
IDS
| 2件: Metabolic pathways Metabolic pathways, Lysosome | D11812
D11812
|
Pabinafusp alfa
| 1件: 19 19 |
19 |
IDUA
| 2件: Metabolic pathways Metabolic pathways, Lysosome | D04670
D04670
|
Laronidase
| 2件: 19 19, 256 |
20 |
LIPA
| 2件: Steroid biosynthesis Steroid biosynthesis, Lysosome | D10377
D10377
|
Sebelipase alfa
| 1件: 19 19 |
21 |
ARSB
| 2件: Metabolic pathways Metabolic pathways, Lysosome | D06565
D06565
|
Galsulfase
| 1件: 19 19 |
22 |
MAN2B1
| 2件: Other glycan degradation Other glycan degradation, Lysosome | D11024
D11024
|
Velmanase alfa
| 1件: 19 19 |
23 |
SMPD1
| 5件: Sphingolipid metabolism Sphingolipid metabolism, Metabolic pathways, Sphingolipid signaling pathway, Lysosome, Necroptosis | D10820
D10820
|
Olipudase alfa
| 1件: 19 19 |